limit dextrin-glycogenin => ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl) glycogenin
limit dextrin-glycogenin dimer → ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl)GYG dimer
- Reactome
- R-HSA-71552
- Compartment
- cytosol
- Rhea
- None recorded
Inputs
- limit dextrin-glycogenin dimerR-HSA-453336, cytosol
Outputs
- ((1,6)-alpha-glucosyl)poly((1,4)-alpha-glucosyl)GYG dimerR-HSA-453350, cytosol
Catalysed by
- 4-alpha-glucanotransferase activity of AGL [cytosol]EC 2.4.1.25; UniProt P35573
Literature
- Glycogen debranching enzyme: purification, antibody characterization, and immunoblot analyses of type III glycogen storage disease. Am J Hum Genet, 1988
- Mutations in exon 3 of the glycogen debranching enzyme gene are associated with glycogen storage disease type III that is differentially expressed in liver and muscle. J Clin Invest, 1996